CONGENITAL TOOTH AGENESIS AND ECTODERMAL DYSPLASIAS
Agenesis of one or a few teeth is common in the population, while congenitally missing six or more teeth (oligodontia) is relatively uncommon. Hypodontia can be an isolated condition or part of a syndrome, of which the various ectodermal dysplasias are among the most common. Hypohidrotic ectodermal dysplasia is the best known, and the best described, form of ectodermal dysplasia and boys with this diagnosis miss an average of 22 permanent teeth. In addition, manifestations are seen in other tissues, such as hair, skin and exocrine glands, and this requires multidisciplinary follow-up and treatment. The dental team has an important and challenging role in both follow-up and treatment of people of all ages with ectodermal dysplasia.